WP_KREBS_CYCLE_DISORDERS Return to index
Order Gene Description ref_hepatocyte HepG2 HepG2.C3A HuH.7 SNU475 THLE liver
1 SUCLG2 Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial [1] -0.88[2] -0.94[3] -1.28[4] -1.73[5] -0.99[6] -0.32[7]
2 SUCLG1 Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial -0.50[8] -0.51[9] 0.41[10] -1.02[11] -0.67[12] -0.82[13]
3 FH Fumarate hydratase, mitochondrial [14] -0.36[15] -0.71[16] -0.49[17] 0.30[18] -0.13[19] -0.09[20]
4 DLST Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial 1.66[21] 1.60[22] 0.54[23] 1.43[24] 1.61[25] -0.78[26]
5 DHTKD1 Probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial -0.39[27] -0.73[28] 0.56[29] 0.76[30] -0.60[31] 2.24[32]
6 SUCLA2 Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial [33] 0.35[34] 0.91[35] -0.08[36] 0.21[37] 0.91[38] -0.46[39]
7 PDHX Pyruvate dehydrogenase protein X component, mitochondrial [40] 0.65[41] 1.08[42] 1.04[43] 0.87[44] 0.32[45] -0.07[46]

[1]
ref_hepatocyte SUCLG2
Mean 52.6
Standard deviation 48
Values 14 1.3e+02 71 15 33
[2]
HepG2 SUCLG2
Mean 27.4
Standard deviation 5.7
Values 31 23
[3]
HepG2.C3A SUCLG2
Mean 34.7
Standard deviation 8.9
Values 41 28
[4]
HuH.7 SUCLG2
Mean 26.2
Standard deviation 0.91
Values 26 26 27
[5]
SNU475 SUCLG2
Mean 13.3
Standard deviation 5.2
Values 9.7 17
[6]
THLE SUCLG2
Mean 23.8
Standard deviation 4.1
Values 21 27
[7]
liver SUCLG2
Mean 69.9
Standard deviation 18
Values 48 63 77 91
[8]
ref_hepatocyte SUCLG1
Mean 51.8
Standard deviation 25
Values 25 71 85 36 42
[9]
HepG2 SUCLG1
Mean 35
Standard deviation 6.7
Values 40 30
[10]
HepG2.C3A SUCLG1
Mean 46
Standard deviation 6.9
Values 51 41
[11]
HuH.7 SUCLG1
Mean 82.9
Standard deviation 9.5
Values 94 78 77
[12]
SNU475 SUCLG1
Mean 21.5
Standard deviation 1.6
Values 20 23
[13]
THLE SUCLG1
Mean 29.3
Standard deviation 2.7
Values 27 31
[14]
liver SUCLG1
Mean 48.5
Standard deviation 38
Values 14 18 89 73
[15]
ref_hepatocyte FH
Mean 43.1
Standard deviation 38
Values 8.7 78 91 17 21
[16]
HepG2 FH
Mean 32
Standard deviation 8
Values 38 26
[17]
HepG2.C3A FH
Mean 33.4
Standard deviation 7.2
Values 39 28
[18]
HuH.7 FH
Mean 37.1
Standard deviation 6.3
Values 43 31 38
[19]
SNU475 FH
Mean 44.6
Standard deviation 4.8
Values 41 48
[20]
THLE FH
Mean 35.3
Standard deviation 6.3
Values 31 40
[21]
liver FH
Mean 67.3
Standard deviation 23
Values 42 55 82 90
[22]
ref_hepatocyte DLST
Mean 19.4
Standard deviation 4.5
Values 24 19 22 12 20
[23]
HepG2 DLST
Mean 58.7
Standard deviation 1.6
Values 58 60
[24]
HepG2.C3A DLST
Mean 74.5
Standard deviation 3.3
Values 72 77
[25]
HuH.7 DLST
Mean 34.1
Standard deviation 5.6
Values 39 28 36
[26]
SNU475 DLST
Mean 43.8
Standard deviation 3.5
Values 41 46
[27]
THLE DLST
Mean 53.2
Standard deviation 2.1
Values 52 55
[28]
liver DLST
Mean 18.7
Standard deviation 14
Values 28 33 6.4 6.7
[29]
ref_hepatocyte DHTKD1
Mean 12.7
Standard deviation 14
Values 3.3 36 18 1.9 4.8
[30]
HepG2 DHTKD1
Mean 9.3
Standard deviation 0.5
Values 8.9 9.7
[31]
HepG2.C3A DHTKD1
Mean 9.71
Standard deviation 0.076
Values 9.7 9.8
[32]
HuH.7 DHTKD1
Mean 22.7
Standard deviation 3.1
Values 23 19 25
[33]
SNU475 DHTKD1
Mean 18.2
Standard deviation 3.3
Values 16 20
[34]
THLE DHTKD1
Mean 7.53
Standard deviation 1.2
Values 6.7 8.4
[35]
liver DHTKD1
Mean 99.9
Standard deviation 9.7
Values 88 1.1e+02 97 1.1e+02
[36]
ref_hepatocyte SUCLA2
Mean 11.9
Standard deviation 8.1
Values 5.1 9.7 5 24 16
[37]
HepG2 SUCLA2
Mean 14.5
Standard deviation 6.2
Values 19 10
[38]
HepG2.C3A SUCLA2
Mean 28.3
Standard deviation 6.8
Values 33 23
[39]
HuH.7 SUCLA2
Mean 13.6
Standard deviation 0.97
Values 15 13 13
[40]
SNU475 SUCLA2
Mean 11.5
Standard deviation 1.5
Values 10 13
[41]
THLE SUCLA2
Mean 20.1
Standard deviation 0.15
Values 20 20
[42]
liver SUCLA2
Mean 14.4
Standard deviation 5.4
Values 8.4 11 18 20
[43]
ref_hepatocyte PDHX
Mean 11.4
Standard deviation 4.3
Values 6.9 10 8.2 15 17
[44]
HepG2 PDHX
Mean 17.1
Standard deviation 5.7
Values 21 13
[45]
HepG2.C3A PDHX
Mean 30.4
Standard deviation 1.9
Values 32 29
[46]
HuH.7 PDHX
Mean 28.3
Standard deviation 3.1
Values 30 25 30
[47]
SNU475 PDHX
Mean 17.6
Standard deviation 1.9
Values 19 16
[48]
THLE PDHX
Mean 12.8
Standard deviation 1.1
Values 12 14
[49]
liver PDHX
Mean 18
Standard deviation 6.9
Values 10 14 24 24